Quick Answer: What Foods Do People With Phenylketonuria Have To Avoid?

What foods are phenylalanine found in?

Phenylalanine occurs naturally in many protein-rich foods, such as milk, eggs and meat.

Phenylalanine is also sold as a dietary supplement..

What triggers phenylketonuria?

Causes of phenylketonuria PKU is an inherited condition caused by a defect in the PAH gene. The PAH gene helps create phenylalanine hydroxylase, the enzyme responsible for breaking down phenylalanine. A dangerous buildup of phenylalanine can occur when someone eats high-protein foods, such as eggs and meat.

What foods do not contain phenylalanine?

Foods such as meat, fish, eggs, milk, cheese, nuts and pulses are excluded as they contain high levels of phenylalanine. Vegetables and fruit are allowed in measured amounts only! Special low protein bread, pasta, biscuits and flour are used to supplement the diet and ensure adequate calorie intake.

Why is phenylalanine in Coke?

Phenylalanine occurs naturally in many protein-rich foods, such as milk, eggs and meat. Phenylalanine is also sold as a dietary supplement. The artificial sweetener aspartame (Equal, NutraSweet), which is added to many medications, diet foods and diet sodas, contains phenylalanine.

Can you grow out of PKU?

A person with PKU does not outgrow it and must stay on the diet for life.

Can PKU babies breastfeed?

Years ago PKU was an absolute contraindication for breastfeeding, but with more research on the disease and the breast milk components, it is now strongly suggested to breastfeed a PKU baby along with his or her special phenylalanine free formula under close supervision from a dietitian and experienced breastfeeding …

What foods can you eat if you have PKU?

PKU DietMeat, eggs, and fish.Bread, noodles, and wheat products.Nuts, peas, and beans (and products made from these foods).Milk and cheese.Chocolate.

How do you prevent phenylketonuria?

PreventionFollow a low-phenylalanine diet. Women with PKU can prevent birth defects by sticking to or returning to a low-phenylalanine diet before becoming pregnant. … Consider genetic counseling.

What foods do not contain protein?

The following are low-protein foods:all fruits, except dried fruits.all vegetables, except peas, beans, and corn.many sources of healthful fats, such as olive oil and avocados.herbs and spices.

Can phenylketonuria be cured?

There is no cure for PKU, but treatment can prevent intellectual disabilities and other health problems. A person with PKU should receive treatment at a medical center that specializes in the disorder.

How does phenylketonuria affect the body?

Phenylketonuria (PKU) is a treatable disorder that affects the way the body processes protein. Children with PKU cannot use a part of the protein called phenylalanine. If left untreated, phenylalanine builds up in the bloodstream and causes brain damage.

What is the life expectancy of someone with PKU?

PKU does not shorten life expectancy, with or without treatment. Newborn screening for PKU is required in all 50 states.

Why is phenylalanine in food?

Phenylalanine is an amino acid found in many foods and used by your body to produce proteins and other important molecules. It has been studied for its effects on depression, pain and skin disorders. This article tells you all you need to know about phenylalanine, including its benefits, side effects and food sources.

Why is phenylalanine toxic to the brain?

The high plasma phenylalanine concentrations increase phenylalanine entry into brain and restrict the entry of other large neutral amino acids. In the literature, emphasis has been on high brain phenylalanine as the pathological substrate that causes mental retardation.

How do PKU patients get protein?

Today, the major source of dietary protein for those with PKU consists of mixtures of synthetic AA devoid of phe and a small amount of dietary protein from fruits and vegetables to provide phe.